Congenital stenosis and stricture of bile ducts

This code represents a birth defect characterized by an abnormal narrowing or obstruction of the bile ducts, which are tubes that carry bile from the liver and gallbladder to the small intestine. This congenital anomaly can impede bile flow, leading to jaundice, liver damage, and malabsorption.

Use this code for patients diagnosed with a congenital narrowing or stricture of any part of the biliary tree. Documentation should clearly state the congenital nature of the stenosis or stricture, often identified in infancy or early childhood due to symptoms like persistent jaundice or acholic stools.

• Differentiate from acquired strictures (e.g., post-surgical, inflammatory) which are coded elsewhere.
• Ensure documentation specifies "congenital" to support this code.
• Consider sequencing with codes for associated conditions like biliary atresia if present, as this code may be a component of a broader diagnosis.