Congenital absence, atresia and stenosis of duodenum

This code signifies a birth defect characterized by the complete absence (agenesis), complete obstruction (atresia), or significant narrowing (stenosis) of the duodenum, the first part of the small intestine. These conditions prevent the normal passage of digestive contents from the stomach into the jejunum.

Use this code for documented cases of congenital duodenal agenesis, atresia, or stenosis identified at birth or shortly thereafter. This diagnosis is typically confirmed by imaging studies (e.g., abdominal X-ray showing a "double bubble" sign, ultrasound) and clinical presentation such as bilious vomiting in a neonate.

• Differentiate from acquired duodenal stenosis, which would be coded elsewhere.
• Always review documentation for laterality if applicable, though duodenal defects are typically midline.
• Consider sequencing with codes for associated congenital anomalies, as these often co-occur (e.g., Down syndrome, other gastrointestinal malformations).