Bicuspid aortic valve

This code identifies a congenital heart defect where the aortic valve has only two leaflets (cusps) instead of the normal three. This structural abnormality can lead to various hemodynamic consequences, including aortic stenosis or regurgitation, and is often associated with other cardiovascular anomalies.

Assign this code when documentation explicitly states the presence of a bicuspid aortic valve, typically identified through echocardiography or other imaging studies. It is appropriate for both symptomatic and asymptomatic individuals diagnosed with this congenital malformation.

• Always confirm the diagnosis of a bicuspid aortic valve from physician documentation, such as cardiology notes or imaging reports.
• Code any associated complications, such as aortic stenosis (I35.0) or aortic regurgitation (I35.1), in addition to this code.
• Do not confuse with acquired aortic valve conditions; this code specifically denotes a congenital anomaly.