Aortopulmonary septal defect

This code represents a congenital heart defect characterized by an abnormal communication between the aorta and the pulmonary artery, allowing blood to shunt between the two great vessels. This defect results from incomplete septation of the truncus arteriosus during fetal development.

Use this code for documented cases of aortopulmonary window or aortopulmonary fistula. Documentation should clearly indicate the presence of this specific congenital anomaly, typically identified through echocardiography or cardiac catheterization.

• Differentiate from patent ductus arteriosus (PDA), which is a separate condition (Q25.0).
• Code any associated congenital heart defects separately, if documented.
• Ensure documentation specifies "aortopulmonary septal defect" or "aortopulmonary window" to support this diagnosis.