Complete atrioventricular septal defect

This code represents a severe congenital heart defect characterized by a large opening between all four chambers of the heart, involving both the atrial and ventricular septa, and a common atrioventricular valve. This malformation results in significant shunting of blood and often leads to heart failure and pulmonary hypertension if uncorrected.

Assign this code for patients diagnosed with a complete atrioventricular septal defect, also known as complete atrioventricular canal defect or endocardial cushion defect. Documentation should clearly specify the complete nature of the defect, differentiating it from partial forms. This code is typically used for initial diagnosis and subsequent encounters related to management of the condition.

• Differentiate carefully between complete and partial atrioventricular septal defects; partial defects are coded elsewhere.
• Always review operative reports and cardiology notes for precise anatomical descriptions of the defect.
• Consider sequencing this code as the primary diagnosis when it is the main reason for the encounter, especially for surgical repair or initial evaluation.