Partial atrioventricular septal defect

This code identifies a congenital heart defect characterized by incomplete fusion of the atrial and ventricular septa, along with abnormalities of the atrioventricular valves, typically a cleft mitral valve. It results in a communication between the atria and ventricles, leading to left-to-right shunting. This defect is a milder form of atrioventricular septal defect (AVSD).

Use this code for patients diagnosed with a partial atrioventricular canal defect, often identified during fetal echocardiography or in infancy/childhood due to symptoms like heart murmur or heart failure. Documentation should clearly specify "partial" or "incomplete" AVSD, distinguishing it from complete forms.

• Ensure documentation specifies "partial" to differentiate from complete AVSD or other septal defects.
• Do not confuse with isolated atrial septal defects (ASD) or ventricular septal defects (VSD).
• Code any associated cardiac anomalies or complications, such as pulmonary hypertension, separately.