Microtia

This code represents a congenital malformation characterized by an underdeveloped or abnormally formed external ear (pinna). It can range in severity from a slightly small ear to complete absence of the auricle, often accompanied by a narrowed or absent ear canal. This condition typically affects one ear but can be bilateral.

Use this code when documentation clearly indicates a diagnosis of microtia, regardless of the specific grade or severity. This applies to newborns, infants, children, and adults diagnosed with this congenital anomaly. Supporting documentation includes physician notes, audiograms, imaging reports (e.g., CT scans), and genetic testing results.

• Do not confuse this with anotia (complete absence of the external ear), which has a separate code.
• Specify laterality (right, left, or bilateral) if documented, using the appropriate subclassification.
• Code any associated conditions, such as atresia of the external auditory canal, separately.