Fournier disease of vagina and vulva

This code represents Fournier gangrene specifically affecting the female external genitalia, including the vagina and vulva. It is a rare, rapidly progressive, and life-threatening necrotizing fasciitis of the perineum, characterized by thrombosis of subcutaneous vessels and subsequent gangrene.

Use this code when documentation explicitly states Fournier gangrene involving the vagina and/or vulva. This diagnosis is typically supported by clinical findings of severe pain, erythema, swelling, crepitus, and necrosis in the affected area, often requiring surgical debridement.

• Ensure documentation clearly specifies "Fournier disease" or "Fournier gangrene" and the involvement of the vagina/vulva.
• Do not code this with gangrene due to diabetes mellitus (E08-E13 with .52) as per the Excludes1 note.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter, especially for surgical debridement.