Priapism due to disease classified elsewhere

This code signifies a prolonged, painful erection (priapism) that is not caused by trauma or medication, but rather is a symptom or complication of an underlying systemic disease. This condition is typically ischemic, meaning blood is trapped in the penis, leading to tissue damage if not promptly treated.

Assign this code when documentation clearly links priapism to a specific systemic condition, such as sickle cell anemia, leukemia, or a neurological disorder. The medical record must explicitly state the underlying disease causing the priapism, not just the priapism itself.

• Always sequence the underlying systemic disease first, as this code is a manifestation code.
• Do not use this code for priapism induced by drugs or trauma; specific codes exist for those etiologies.
• Ensure the documentation specifies "due to" or "secondary to" the underlying disease to support the causal link.