Nephrotic syndrome with dense deposit disease

This code represents a specific type of nephrotic syndrome characterized by the abnormal accumulation of electron-dense material within the glomerular basement membrane. This deposition leads to significant proteinuria, hypoalbuminemia, edema, and hyperlipidemia, which are the hallmarks of nephrotic syndrome. It is a rare, chronic kidney disease often progressing to end-stage renal disease.

Use this code when the patient's medical record clearly documents a diagnosis of nephrotic syndrome and specifies dense deposit disease as the underlying cause. This diagnosis is typically confirmed through renal biopsy findings demonstrating characteristic dense deposits. Documentation should explicitly link the nephrotic syndrome to dense deposit disease.

• Ensure the documentation explicitly states "dense deposit disease" as the etiology of the nephrotic syndrome.
• Do not confuse this with other forms of glomerulonephritis or nephrotic syndrome without a specified cause.
• Code any associated complications of nephrotic syndrome, such as acute kidney injury or thrombosis, in addition to this code.