Juvenile rheumatoid arthritis w systemic onset, l shoulder

This code identifies a specific type of chronic inflammatory arthritis affecting children, characterized by systemic symptoms such as fever, rash, and lymphadenopathy, in addition to joint inflammation. Specifically, it indicates that the left shoulder joint is affected by this systemic onset juvenile idiopathic arthritis.

Apply this code when documentation clearly states a diagnosis of systemic onset juvenile rheumatoid arthritis (now often referred to as systemic juvenile idiopathic arthritis) with involvement of the left shoulder. Supporting documentation should include physician notes detailing the systemic features and confirmation of left shoulder arthritis.

• Ensure documentation specifies "systemic onset" and not another subtype of juvenile idiopathic arthritis.
• Verify the laterality of the affected joint; this code is specific to the left shoulder.
• Do not confuse with other forms of juvenile idiopathic arthritis (e.g., oligoarticular, polyarticular) which have distinct codes.