Atrophoderma of Pasini and Pierini

Atrophoderma of Pasini and Pierini is a rare, benign, acquired dermal atrophy characterized by single or multiple, well-demarcated, slightly depressed, hyperpigmented or bluish-brown patches, typically on the trunk. The skin lesions are usually asymptomatic, lack induration, and do not involve the subcutaneous tissue. It is considered a superficial variant of localized scleroderma (morphea) without significant inflammation or sclerosis.

This code is used when documentation explicitly identifies the diagnosis as "Atrophoderma of Pasini and Pierini." It applies to patients presenting with the characteristic depressed, hyperpigmented patches without evidence of systemic involvement or deeper tissue sclerosis. Supporting documentation should include a dermatologist's diagnosis based on clinical examination, and potentially a skin biopsy confirming dermal atrophy without significant inflammation or collagen thickening.

• Differentiate from other forms of localized scleroderma (morphea); this code is specific to the Pasini and Pierini variant.
• Ensure documentation clearly states "Atrophoderma of Pasini and Pierini" to avoid confusion with other atrophic skin conditions.
• Do not use for generalized or systemic scleroderma, which involve different ICD-10-CM codes.