Cafe au lait spots

This code represents hyperpigmented macules or patches on the skin, typically light brown in color, resembling coffee with milk. These lesions are usually benign but can be indicative of underlying genetic disorders when multiple or large.

Assign this code when documentation specifies the presence of cafe au lait spots. This is often used in pediatric dermatology or genetics clinics. Documentation should clearly identify the lesions as cafe au lait spots, not just general hyperpigmentation.

• Do not use this code for general hyperpigmentation (e.g., freckles, sunspots) without specific mention of cafe au lait spots.
• Consider additional codes for underlying conditions like Neurofibromatosis type 1 (NF1) if multiple or large spots are present and diagnosed.
• Ensure the provider's documentation differentiates cafe au lait spots from other pigmented lesions.