Steatocystoma multiplex

This code represents a rare, benign, autosomal dominant disorder characterized by the development of numerous asymptomatic dermal cysts. These cysts, known as steatocystomas, are typically filled with an oily, yellowish fluid and often contain hair shafts. They commonly appear on the trunk, neck, and proximal extremities.

Use this code for patients diagnosed with steatocystoma multiplex, a condition involving multiple sebaceous cysts. Documentation should clearly indicate the presence of multiple steatocystomas, often confirmed by clinical examination and sometimes biopsy. This code is appropriate for both initial diagnosis and subsequent encounters related to the management of this condition.

• Differentiate from solitary steatocystoma, which would be coded differently.
• Ensure documentation specifies "multiplex" to support the use of this code.
• Consider additional codes for any associated complications, such as infection or rupture, if present.