Central centrifugal cicatricial alopecia

This diagnosis code identifies a specific type of progressive, permanent hair loss primarily affecting the crown and vertex of the scalp. It is characterized by inflammation and scarring of the hair follicles, leading to irreversible alopecia. The condition typically starts in the central scalp and spreads centrifugally.

Assign this code when documentation clearly indicates a diagnosis of central centrifugal cicatricial alopecia (CCCA). This diagnosis is often made based on clinical presentation, trichoscopy, and sometimes confirmed by scalp biopsy showing perifollicular inflammation and fibrosis. Use this code for patients presenting with progressive, scarring alopecia in the characteristic pattern.

• Ensure documentation specifies "cicatricial" (scarring) to differentiate from non-scarring alopecias.
• Do not confuse with other forms of cicatricial alopecia, such as lichen planopilaris or discoid lupus erythematosus, which have distinct codes.
• Consider sequencing with codes for any associated symptoms or underlying conditions, if applicable and documented.