Other pemphigus

This code represents various rare forms of pemphigus that do not fit into more specific categories like pemphigus vulgaris or foliaceus. These are autoimmune blistering diseases affecting the skin and/or mucous membranes, characterized by acantholysis. The specific clinical presentation can vary depending on the subtype.

Use this code for documented cases of pemphigus that are explicitly identified as "other specified pemphigus" or a less common variant not otherwise classified. This includes conditions such as pemphigus erythematosus (Senear-Usher syndrome), pemphigus vegetans, or drug-induced pemphigus when the specific drug is also coded. Documentation should clearly state the type of pemphigus and rule out more common forms.

• Ensure the physician documentation specifies a type of pemphigus that is not pemphigus vulgaris (L10.0), pemphigus vegetans (L10.1), pemphigus foliaceus (L10.2), or Brazilian pemphigus (L10.3).
• If drug-induced, also code the adverse effect of the drug (T36-T50 with 5th or 6th character 5).
• Avoid using this code if a more specific pemphigus code is available and documented.