Other hypertrophic cardiomyopathy

This code represents a primary myocardial disorder characterized by unexplained left ventricular hypertrophy, often asymmetric, in the absence of other cardiac or systemic diseases that could cause such hypertrophy (e.g., hypertension, aortic stenosis). It involves a thickening of the heart muscle, particularly the septum, which can impede blood flow and lead to various symptoms and complications.

Use this code when documentation specifies hypertrophic cardiomyopathy that does not fall under obstructive, nonobstructive, or apical types. This typically applies to cases where the specific subtype of hypertrophic cardiomyopathy is not further defined or when it presents with atypical features not captured by more specific codes. Supporting documentation includes echocardiogram reports, cardiac MRI findings, and physician notes confirming the diagnosis of hypertrophic cardiomyopathy without further specification.

• Do not use this code if the documentation specifies obstructive hypertrophic cardiomyopathy (I42.1) or nonobstructive hypertrophic cardiomyopathy (I42.2).
• Ensure the medical record clearly indicates hypertrophic cardiomyopathy and that other causes of hypertrophy have been ruled out.
• Consider sequencing this code as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis when it is a co-morbidity affecting treatment or management.