Other Fontan-associated condition

This code represents a range of medical conditions that develop as a consequence of having undergone a Fontan procedure, excluding pulmonary hypertension, plastic bronchitis, protein-losing enteropathy, and thromboembolism. These are often chronic and complex issues affecting various organ systems due to the altered circulation.

Use this code when documentation specifies a Fontan-associated condition that is not otherwise classified to a more specific Fontan-associated code (e.g., I27.83 for pulmonary hypertension). Examples include Fontan-associated liver disease (FALD) or Fontan-associated heart failure not specified as a more precise cardiac diagnosis. Documentation should clearly link the condition to the patient's history of a Fontan procedure.

• Always sequence this code after the primary diagnosis for the specific Fontan-associated condition, if applicable.
• Do not use this code if a more specific Fontan-associated condition code exists (e.g., I27.83, K90.41, J98.01, I26.01, I26.90).
• Ensure the medical record explicitly states the patient has a history of a Fontan procedure and the condition is a direct sequela.