Other rheumatic mitral valve diseases

This code represents various non-rheumatic mitral valve disorders that are secondary to a rheumatic fever etiology, but do not fall into the categories of mitral stenosis, insufficiency, or prolapse. These conditions involve structural or functional abnormalities of the mitral valve apparatus caused by prior rheumatic heart disease.

Use this code when documentation specifies a rheumatic mitral valve disease other than stenosis, insufficiency, or prolapse. Examples include rheumatic mitral valve calcification, annular dilation, or leaflet thickening without significant stenosis or regurgitation. The medical record must clearly link the mitral valve pathology to a history of rheumatic fever.

• Do not use this code for non-rheumatic mitral valve conditions; ensure a clear link to rheumatic etiology.
• Always sequence a code for the underlying rheumatic fever (e.g., I00) if it is active or if it is important for the clinical picture.
• Differentiate carefully from I05.0 (rheumatic mitral stenosis), I05.1 (rheumatic mitral insufficiency), and I05.2 (rheumatic mitral stenosis with insufficiency).