Other acute rheumatic heart disease

This code describes acute rheumatic heart disease affecting cardiac structures other than the mitral or aortic valves, or involving multiple valves without specific mention of mitral or aortic. It signifies an inflammatory process of the heart resulting from an acute rheumatic fever episode. This condition can lead to permanent heart damage if not properly managed.

Use this code when documentation specifies acute rheumatic carditis affecting the tricuspid or pulmonary valves, or when multiple valves are involved in acute rheumatic heart disease without further specification. It is appropriate when the patient presents with symptoms and signs of acute inflammation of the heart following a streptococcal infection. Documentation should clearly state "acute rheumatic heart disease" and specify the affected valves if not mitral or aortic, or indicate multiple valve involvement.

• Do not use this code if the documentation specifies acute rheumatic mitral or aortic valve disease; use the more specific codes.
• Always code the underlying acute rheumatic fever (I00) first, followed by this code to indicate the cardiac manifestation.
• Ensure the documentation clearly distinguishes between acute and chronic rheumatic heart disease, as different codes apply.