Optic nerve hypoplasia, bilateral

This code signifies a congenital underdevelopment of both optic nerves, resulting in varying degrees of visual impairment. It is a non-progressive condition where the optic disc appears smaller than normal due to a reduced number of optic nerve axons.

Apply this code when documentation explicitly states bilateral optic nerve hypoplasia. This diagnosis is typically made during an ophthalmic examination, often in infancy or early childhood, and supported by findings such as small optic discs, peripapillary pigmentary changes, and visual field defects.

• Ensure documentation specifies "bilateral" involvement; otherwise, use the appropriate unilateral code.
• Do not confuse with optic atrophy (H47.2x), which is a degeneration of a previously developed optic nerve.
• Code any associated visual impairment or blindness separately, if documented.