Retinopathy of prematurity, stage 0, unspecified eye

This code signifies the earliest, most benign form of retinopathy of prematurity (ROP), characterized by the absence of a demarcation line or ridge between vascularized and avascular retina. It indicates that the retina has not yet begun to develop abnormal blood vessel growth, but the premature infant is at risk for progression.

Use this code for premature infants diagnosed with ROP who show no signs of disease (stage 0) in an unspecified eye. This diagnosis is typically made during routine ophthalmological screening examinations of premature infants. Documentation should explicitly state "retinopathy of prematurity, stage 0" without specifying laterality.

• Do not use this code if any stage of ROP (stage 1 or higher) is identified in either eye; instead, code the highest stage present.
• If laterality is documented (e.g., "stage 0, right eye"), use the more specific codes H35.111 or H35.112.
• This code is often used in conjunction with codes for prematurity (P07.xx) and other conditions associated with premature birth.