Multifocal motor neuropathy

This code represents a rare, acquired, immune-mediated peripheral neuropathy characterized by slowly progressive, asymmetric muscle weakness and atrophy, primarily affecting the distal upper limbs. It involves persistent conduction block in motor nerves without significant sensory involvement.

Use this code for patients diagnosed with multifocal motor neuropathy based on clinical presentation, electrophysiological studies demonstrating multifocal motor conduction blocks, and exclusion of other motor neuron diseases. Documentation should clearly indicate the diagnosis and the absence of significant sensory deficits.

• Differentiate from amyotrophic lateral sclerosis (ALS) or other motor neuron diseases; electrophysiological findings are key.
• Ensure documentation specifies "multifocal" and "motor" to distinguish from other neuropathies.
• Consider sequencing with codes for associated autoimmune conditions if applicable.