Dravet syndrome, intractable, without status epilepticus

This code represents Dravet syndrome, a severe form of epilepsy characterized by prolonged, febrile, and afebrile seizures, often beginning in infancy. The "intractable" designation indicates that the seizures are refractory to conventional antiepileptic drug therapy. This specific code applies when the patient is not currently experiencing status epilepticus.

Use this code for patients with a confirmed diagnosis of Dravet syndrome whose seizures are difficult to control despite treatment. Documentation should clearly state the diagnosis of Dravet syndrome, the intractable nature of the seizures, and explicitly rule out the presence of status epilepticus at the time of encounter. This code is appropriate for ongoing management of this chronic, severe condition.

• Ensure documentation specifies "intractable" and "without status epilepticus" to support this precise code.
• Do not confuse with other epilepsy codes that do not specify Dravet syndrome or intractability.
• Always sequence this code as the primary diagnosis when it is the focus of the encounter.