Concentric sclerosis [Balo] of central nervous system

This code identifies a rare, aggressive demyelinating disease of the central nervous system characterized by alternating layers of preserved and demyelinated white matter, forming concentric rings. It is considered a variant of multiple sclerosis, often presenting with rapid neurological deterioration.

Assign this code when documentation explicitly states a diagnosis of concentric sclerosis or Balo's concentric sclerosis. This diagnosis is typically made based on characteristic imaging findings (MRI showing concentric lesions) and clinical presentation, often confirmed by biopsy.

• Ensure documentation clearly specifies "concentric sclerosis" or "Balo's disease" to differentiate from other demyelinating conditions.
• Do not confuse with other forms of multiple sclerosis (e.g., relapsing-remitting, primary progressive) unless concentric sclerosis is specifically diagnosed.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter or hospitalization.