Primary progressive apraxia of speech

This code represents a neurological disorder characterized by a gradual and isolated impairment of speech motor planning and programming, without significant aphasia or other cognitive deficits initially. Patients experience increasing difficulty articulating words and sequencing speech sounds, despite understanding language and knowing what they want to say. It is a form of primary progressive neurological disease affecting speech production.

Use this code for patients diagnosed with primary progressive apraxia of speech (PPAOS) based on neurological evaluation and speech-language pathology assessment. Documentation should clearly indicate a progressive, isolated apraxia of speech as the primary and presenting symptom, differentiating it from other forms of aphasia or dysarthria.

• Differentiate from other progressive speech disorders like dysarthria (R47.1) or primary progressive aphasia (G31.01, G31.09).
• Ensure documentation specifies "primary progressive" to support this specific diagnosis.
• Consider sequencing this code as the primary diagnosis when PPAOS is the main reason for the encounter.