Stiff-man syndrome

This code represents Stiff-Person Syndrome (SPS), a rare, progressive neurological disorder characterized by fluctuating muscle rigidity and painful spasms, primarily affecting the trunk and limbs. The rigidity is often precipitated by sudden movement, noise, or emotional stress, and can lead to an abnormal, often lordotic, posture.

Use this code for patients definitively diagnosed with Stiff-Person Syndrome. Documentation should clearly describe the characteristic muscle stiffness, spasms, and the progressive nature of the condition, often accompanied by electromyography (EMG) findings or positive autoantibody tests (e.g., anti-GAD65 antibodies).

• Ensure documentation specifies "Stiff-Person Syndrome" (formerly Stiff-Man Syndrome) to avoid confusion with other rigidity disorders.
• Do not confuse with generalized tetanus or dystonia, which have distinct etiologies and clinical presentations.
• Code any associated neurological complications or autoimmune conditions separately, if documented.