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ICD-10-CM E71 — Disord of branched-chain amino-ac… | Codelle

E71

ICD-10-CM

Disord of branched-chain amino-acid metab & fatty-acid metab

Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

Code Hierarchy

Subcodes (6)

E71.0Maple-syrup-urine disease

E71.1Other disorders of branched-chain amino-acid metabolism

E71.2Disorder of branched-chain amino-acid metabolism, unsp

E71.3Disorders of fatty-acid metabolism

E71.4Disorders of carnitine metabolism

E71.5Peroxisomal disorders

Same Category

E71.0Maple-syrup-urine disease E71.1Other disorders of branched-chain amino-acid metabolism E71.11Branched-chain organic acidurias E71.110Isovaleric acidemia E71.1113-methylglutaconic aciduria E71.118Other branched-chain organic acidurias E71.12Disorders of propionate metabolism E71.120Methylmalonic acidemia E71.121Propionic acidemia E71.128Other disorders of propionate metabolism

+5 more in this category