Sarcoidosis of lung

This code signifies a chronic inflammatory disease characterized by the growth of tiny collections of inflammatory cells (granulomas) in the lungs. It is a systemic disorder, but this specific code indicates that the primary or most significant manifestation is within the pulmonary system. The granulomas can affect lung function and lead to various respiratory symptoms.

Apply this code when documentation explicitly states a diagnosis of sarcoidosis primarily affecting the lungs. This includes cases where lung involvement is the initial presentation or the predominant site of disease. Supporting documentation would include biopsy results confirming non-caseating granulomas, imaging findings (e.g., chest X-ray, CT scan) consistent with pulmonary sarcoidosis, and clinical assessment.

• Do not use this code if sarcoidosis is present in other organs without specific mention of lung involvement, or if lung involvement is secondary to a more prominent systemic manifestation coded elsewhere.
• Consider additional codes for specific pulmonary complications, such as pulmonary fibrosis (J84.10) or pulmonary hypertension (I27.20), if documented.
• Ensure the documentation clearly distinguishes between sarcoidosis of the lung and other interstitial lung diseases.