Sickle-cell/Hb-C disease with splenic sequestration

This code signifies a specific type of sickle cell disease, characterized by the presence of both hemoglobin S and hemoglobin C, complicated by splenic sequestration. Splenic sequestration is a life-threatening acute complication where a large volume of blood pools in the spleen, leading to rapid enlargement of the organ and severe anemia.

Apply this code when documentation explicitly states a diagnosis of sickle cell-hemoglobin C (Hb-C) disease and identifies acute splenic sequestration as a current complication. This typically occurs in pediatric patients but can affect adults. Supporting documentation includes physician notes detailing the diagnosis, clinical signs of splenic enlargement, and laboratory findings consistent with acute anemia.

• Ensure the documentation clearly specifies "Hb-C" type sickle cell disease, not other variants.
• Verify that splenic sequestration is an acute event, not a chronic finding or a history of splenectomy.
• Do not confuse with other sickle cell crises; this code is specific to splenic sequestration.