Benign neoplasm of aortic body and other paraganglia

This code signifies a non-cancerous tumor originating from specialized neuroendocrine cells found in the aortic body or other paraganglia. These paragangliomas are typically slow-growing and do not metastasize, though they can be hormonally active.

Apply this code for documented benign paragangliomas located in the aortic body, carotid body, or other non-adrenal paraganglionic sites. Supporting documentation should clearly state the benign nature and specific anatomical location of the neoplasm.

• Distinguish from malignant paragangliomas (C75.5) which require different coding.
• Ensure documentation specifies "benign" and the paraganglionic origin; otherwise, query the provider.
• Do not use for pheochromocytomas of the adrenal gland, which have distinct codes.