Prolymphocytic leukemia of T-cell type not achieve remission

This code signifies a diagnosis of T-cell prolymphocytic leukemia (T-PLL), a rare and aggressive mature T-cell neoplasm. It indicates that the disease is active and has not yet responded to treatment to achieve remission.

Apply this code when documentation confirms a diagnosis of T-cell prolymphocytic leukemia, and the patient's current disease status is active, without any mention of remission. Supporting documentation includes pathology reports confirming T-PLL and physician notes indicating ongoing disease activity.

• Do not use this code if the patient is in remission; a different code would be required.
• Ensure the documentation specifically states "T-cell type" to differentiate from other prolymphocytic leukemias.
• Verify that the "not having achieved remission" status is clearly documented, as this is a key specificity for this code.