Oth mature T/NK-cell lymph, extrnod and solid organ sites

This code represents a rare group of aggressive lymphomas originating from mature T-lymphocytes or natural killer (NK) cells that are found outside of the lymph nodes and bone marrow, affecting solid organs or other extranodal sites. These are distinct from more common B-cell lymphomas and often present with varied clinical manifestations depending on the affected site.

Use this code for confirmed diagnoses of mature T/NK-cell lymphomas that do not fit more specific classifications and are identified in extranodal locations such as the skin, gastrointestinal tract, liver, or other solid organs. Documentation should clearly specify the T/NK-cell lineage and the extranodal or solid organ involvement, ruling out nodal disease.

• Ensure the pathology report explicitly identifies the lymphoma as a mature T-cell or NK-cell type and specifies an extranodal or solid organ site.
• Do not use this code for lymphomas primarily involving lymph nodes or bone marrow; those have more specific codes.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter, unless a complication or manifestation is being treated.