Mature T/NK-cell lymph, unsp, extrnod and solid organ sites

This code signifies a diagnosis of mature T-cell or NK-cell lymphoma that is not further specified as to its exact type, and which originates or is primarily located outside of the lymph nodes and bone marrow, affecting solid organs or other extranodal sites. These are aggressive cancers of the immune system's T-lymphocytes or natural killer cells.

Use this code when the medical record clearly indicates a diagnosis of mature T/NK-cell lymphoma, but the specific subtype (e.g., anaplastic large cell lymphoma, peripheral T-cell lymphoma, NOS) is not documented, and the disease is confirmed to be extranodal or affecting solid organs. This code is appropriate when the pathologist's report or physician's diagnosis specifies "mature T/NK-cell lymphoma, NOS, extranodal."

• Always seek further specificity regarding the exact subtype of mature T/NK-cell lymphoma if available in the documentation.
• Ensure the documentation explicitly states "extranodal" or involvement of "solid organs" to support the final digit.
• This code is a "not otherwise specified" (NOS) code; avoid using it if a more specific diagnosis is documented.