Peripheral T-cell lymphoma, not elsewhere classified, spleen

This code identifies a rare and aggressive type of non-Hodgkin lymphoma originating from mature T-lymphocytes, specifically when the primary or significant involvement is found in the spleen. It encompasses various subtypes of peripheral T-cell lymphoma that do not fit more specific classifications.

Apply this code when documentation confirms a diagnosis of peripheral T-cell lymphoma, not otherwise specified, with explicit mention of splenic involvement. This is typically supported by pathology reports from splenic biopsies or imaging studies indicating significant splenic disease in the context of this lymphoma.

• Ensure the documentation clearly states "not elsewhere classified" or similar phrasing for the T-cell lymphoma type.
• Verify splenic involvement is explicitly documented, not merely suspected.
• Do not use if a more specific subtype of peripheral T-cell lymphoma (e.g., anaplastic large cell lymphoma) is identified.