Sezary disease, spleen

This code signifies Sezary disease, a rare and aggressive form of cutaneous T-cell lymphoma, specifically when there is documented involvement of the spleen. It indicates systemic spread of the malignant T-cells beyond the skin.

Apply this code when medical record documentation confirms a diagnosis of Sezary disease with evidence of splenic involvement, typically identified through imaging studies (e.g., CT, MRI) or biopsy. This code is appropriate for patients undergoing treatment or surveillance for this specific manifestation of the disease.

• Always ensure documentation explicitly states "Sezary disease" and "spleen involvement."
• Do not use this code for other forms of cutaneous T-cell lymphoma or for Sezary disease without confirmed splenic metastasis.
• Consider sequencing this code after the primary Sezary disease code if a more specific code for Sezary disease without splenic involvement is used.