Sezary disease, intrathoracic lymph nodes

This code signifies a rare and aggressive form of cutaneous T-cell lymphoma, specifically Sezary disease, that has spread to or originated in the lymph nodes located within the chest cavity. It indicates systemic involvement beyond the skin, impacting the intrathoracic lymphatic system.

Use this code when documentation confirms a diagnosis of Sezary disease with evidence of involvement of the intrathoracic lymph nodes. This typically includes findings from imaging studies (e.g., CT scan, PET scan) or biopsy results confirming lymphoma in these specific lymph nodes.

• Ensure documentation clearly specifies "Sezary disease" and "intrathoracic lymph nodes" to support this precise code.
• Do not confuse this with other types of cutaneous T-cell lymphoma or other lymphomas affecting intrathoracic lymph nodes.
• Code any associated skin manifestations or other systemic involvement with additional, appropriate codes.