Mycosis fungoides, extranodal and solid organ sites

This code signifies a diagnosis of Mycosis Fungoides, a type of cutaneous T-cell lymphoma, when it has spread beyond the skin to involve internal organs or other non-lymph node solid tissues. This indicates advanced-stage disease where the malignant T-cells are no longer confined to the integumentary system.

Apply this code when documentation clearly states Mycosis Fungoides with involvement of extranodal sites such as the liver, lungs, gastrointestinal tract, or other solid organs. This is appropriate for patients with systemic manifestations of the disease, confirmed by biopsy or imaging.

• Ensure documentation specifies extranodal and solid organ involvement, not just lymph node involvement.
• Do not confuse with codes for Mycosis Fungoides confined to the skin or involving only lymph nodes.
• Always sequence this code after any underlying cause or primary manifestation if applicable, though for Mycosis Fungoides, this is often the primary diagnosis.