Other non-follicular lymphoma, spleen

This code signifies a malignant lymphoma originating from lymphocytes, but not of follicular type, that is primarily or solely located in the spleen. It encompasses various rare non-follicular lymphoma subtypes affecting the spleen, excluding those with specific codes for other sites or types.

Apply this code when documentation confirms a diagnosis of a non-follicular lymphoma with primary or exclusive involvement of the spleen. This is appropriate when the specific non-follicular subtype (e.g., mantle cell, marginal zone, diffuse large B-cell) is not specified or when the spleen is the only documented site of involvement for such a lymphoma.

• Ensure the documentation explicitly states "spleen" as the primary or sole site of involvement for the non-follicular lymphoma.
• Do not use this code if a more specific code exists for the particular non-follicular lymphoma subtype (e.g., mantle cell lymphoma, splenic marginal zone lymphoma) or if other sites are involved.
• Always sequence this code after any codes for the specific type of non-follicular lymphoma, if known and if the spleen is one of multiple sites.