Burkitt lymphoma, extranodal and solid organ sites

This code signifies a specific type of high-grade B-cell lymphoma, Burkitt lymphoma, when it originates or primarily involves sites outside of the lymph nodes, spleen, or bone marrow. This includes solid organs such as the gastrointestinal tract, kidneys, ovaries, or central nervous system. It is characterized by rapid growth and aggressive behavior.

Use this code when documentation confirms a diagnosis of Burkitt lymphoma and specifies its primary involvement or metastatic spread to extranodal or solid organ sites. This diagnosis is typically established through biopsy and immunohistochemical staining. Supporting documentation should clearly indicate the extranodal location(s) of the tumor.

• Always confirm the specific type of non-Hodgkin lymphoma; do not use this code for other B-cell lymphomas.
• Ensure the documentation explicitly states "extranodal" or identifies a specific solid organ site (e.g., "Burkitt lymphoma of the kidney").
• Sequence this code as the primary diagnosis when it is the reason for the encounter; code any associated symptoms or complications as secondary diagnoses.