Lymphoblastic lymphoma, extrnod and solid organ sites

This code signifies a diagnosis of lymphoblastic lymphoma that has originated or spread to sites outside of the lymphatic system, such as solid organs. Lymphoblastic lymphoma is an aggressive type of non-Hodgkin lymphoma characterized by the rapid proliferation of immature lymphoid cells.

Use this code when documentation clearly indicates a diagnosis of lymphoblastic lymphoma affecting extranodal sites or solid organs. This includes cases where the primary presentation is in a non-lymphoid organ or when there is documented metastatic involvement of solid organs. Supporting documentation should specify the type of lymphoma as lymphoblastic and identify the extranodal or solid organ involvement.

• Ensure the pathology report explicitly states "lymphoblastic lymphoma" and details extranodal or solid organ involvement.
• Do not use this code for lymphoblastic lymphoma confined to lymph nodes; a different subcategory would apply.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter, unless another condition is driving the primary treatment.