Small cell B-cell lymphoma, extranodal and solid organ sites

This code identifies a specific type of non-Hodgkin lymphoma characterized by small B-lymphocytes, originating in sites outside of the lymph nodes or bone marrow, such as the gastrointestinal tract, skin, or other solid organs. It represents a malignant proliferation of small B-cells in extranodal locations.

Assign this code when documentation clearly specifies a diagnosis of small cell B-cell lymphoma confirmed by pathology, with the primary site of involvement being an extranodal or solid organ. This includes cases where the lymphoma is found in organs like the stomach, lung, or salivary glands, rather than in lymphatic tissue.

• Ensure pathology reports confirm "small cell B-cell lymphoma" and specify an extranodal or solid organ site.
• Do not use for follicular lymphoma, mantle cell lymphoma, or other B-cell lymphomas, even if they involve extranodal sites, as these have distinct ICD-10-CM codes.
• Sequence this code as the primary diagnosis when the lymphoma is the reason for the encounter, followed by codes for any associated symptoms or complications.