Gastrointestinal stromal tumor of small intestine

📋Clinical Description

This code signifies a malignant mesenchymal tumor originating from the interstitial cells of Cajal, specifically located within the small intestine. These tumors are characterized by their spindle cell or epithelioid morphology and often express CD117 (KIT) protein.

🎯When to Use

Apply this code when documentation clearly identifies a primary gastrointestinal stromal tumor (GIST) confirmed to be located in the small intestine. This diagnosis is typically established through biopsy and immunohistochemical staining. Use for both initial diagnosis and subsequent encounters related to the GIST.

💡Coding Tips

Ensure the documentation specifies "small intestine" as the primary site; do not use for GISTs of other gastrointestinal organs.
Confirm the tumor is malignant; benign GISTs are coded differently.
Do not confuse with other small intestinal malignancies like adenocarcinoma or lymphoma.

AI-generated reference — verify against official guidelines

Code Hierarchy

▲C49.AGastrointestinal stromal tumor

C49.A3(current)

Same Category

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