Oth interstit pulmon dis with fibrosis in dis classd elswhr

This code signifies interstitial lung disease characterized by fibrosis, where the primary underlying condition causing the pulmonary fibrosis is classified and coded separately. It represents a fibrotic lung process that is secondary to another systemic or localized disease.

Use this code when documentation clearly indicates interstitial pulmonary fibrosis that is a manifestation or complication of another specified disease, such as rheumatoid arthritis, scleroderma, or sarcoidosis. The underlying disease must be coded first, followed by this code to specify the fibrotic lung involvement.

• Always sequence the underlying systemic disease first, as this code is an "in diseases classified elsewhere" code.
• Ensure documentation specifies both the interstitial fibrosis and the causal underlying condition.
• Do not use for idiopathic pulmonary fibrosis (IPF) or other primary interstitial lung diseases.